Incomplete Shone’s Complex with BAV and VSD in Adult Diagnosed by Echocardiography

Qu, MD Yichen; Yang, MD Ya; Xie, MD Jinjie; Li, MD Rongjuan; Zhang, MD Han; Song, MD Li; Wang, MD Yueli; Li, MD Jing

doi:10.37015/AUDT.2021.200017

ADVANCED ULTRASOUND IN DIAGNOSIS AND THERAPY >

2021 , Vol. 5 >Issue 2: 106 - 108

DOI: https://doi.org/10.37015/AUDT.2021.200017

Case Reports

Incomplete Shone’s Complex with BAV and VSD in Adult Diagnosed by Echocardiography

Qu, MD Yichen ,
Yang, MD Ya ,
Xie, MD Jinjie ,
Li, MD Rongjuan ,
Zhang, MD Han ,
Song, MD Li ,
Wang, MD Yueli ,
Li, MD Jing

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Department of Echocardiography, Beijing Anzhen Hospital, Capital Medical University, Beijing, China

Received date: 2020-03-26

Revised date: 2020-06-04

Online published: 2021-06-28

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Abstract

Abstract: The Shone’s complex, defined as a constellation of parachute mitral valve (PMV), supravalvular ring of the left atrium, subaortic stenosis, and aorta coarctation, is a rare entity, which more commonly occurs in its incomplete form. We report the case of a 28-year-old female patient who presented for chest congestion and palpitation with history of congenital mitral valve malformation. Echocardiography revealed the coexistence of PMV, aortic coarctation with bicuspid aortic valve (BAV), and ventricular septum defect (VSD). The patient then received surgical intervention. The diagnosis of Shone’s complex with BAV and VSD made by echocardiography were confirmed later at surgery.

Key words： Bicuspid aortic valve; Ventricular septum defect; Echocardiography

Cite this article

Qu, MD Yichen , Yang, MD Ya , Xie, MD Jinjie , Li, MD Rongjuan , Zhang, MD Han , Song, MD Li , Wang, MD Yueli , Li, MD Jing . Incomplete Shone’s Complex with BAV and VSD in Adult Diagnosed by Echocardiography[J]. ADVANCED ULTRASOUND IN DIAGNOSIS AND THERAPY, 2021 , 5(2) : 106 -108 . DOI: 10.37015/AUDT.2021.200017

References

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