Use of Ultrasound and Digital Subtraction Angiography for Arteriovenous Malformations in a Patient with Klippel-Trenaunay-Weber Syndrome

doi:10.37015/AUDT.2020.200009

Abstract

Abstract:

We report a case of a 21-year-old woman with Klippel-Trenaunay-Weber syndrome (KTWS), a rare congenital syndrome involving capillary malformations, arteriovenous malformations, and soft tissue or bone hypertrophy. For this patient, ultrasound and digital subtraction angiography (DSA) were used to evaluate arteriovenous malformations. Arteriovenous shunts could be identified with both ultrasound and DSA. DSA was able to provide an overall view of the malformed blood vessels, whereas ultrasound was effective in showing the condition of the blood vessel walls and in assessing blood flow velocity. This case suggests that multiple imaging studies may be needed for the diagnosis and treatment of KTWS disease in these patients.

Key words: Klippel-Trenaunay-Weber syndrome (KTWS); Ultrasound; Arteriovenous malformations; Digital subtraction angiography

Zhimei Cheng, BS, Shuai Zhang, PhD, Ping Wang, BS, Hong Zhu, BS, Zhijing Wei, BS, Shi Zhou, BS. Use of Ultrasound and Digital Subtraction Angiography for Arteriovenous Malformations in a Patient with Klippel-Trenaunay-Weber Syndrome. Advanced Ultrasound in Diagnosis and Therapy, 2020, 4(3): 243-247.

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