Sonographic Characteristics of Congenital Pulmonary Airway Malformations in Children: A Report of 21 Cases and Review of Literature

doi:10.37015/AUDT.2018.180812

Abstract

Abstract:

Objective: This study discusses the diagnostic value of ultrasonography for congenital pulmonary airway malformations (CPAM) in children.
Methods: A retrospective analysis was conducted for 21 pathologically confirmed paediatric cases of CPAM by reviewing the ultrasonography images and comparing them with the clinical and pathologic results.
Results: All 21 paediatric cases of CPAM had lesions in unilateral lobes, with five cases involving the left lung and 16 cases involving the right lung. There were six cases with type 1 ultrasonography manifestations, 12 cases with type 2 ultrasonography manifestations and one case with a type 4 ultrasonography manifestation. One case was misdiagnosed as pulmonary sequestration (PS) by ultrasonography, and another case had no abnormalities based on ultrasonography. With respect to the pathologic results, six type 1 (28.6%), 13 type 2 (61.9%) and one type 4 (4.8%) were found, and one type 2 was complicated with PS (4.8%). The ultrasonography diagnoses agreed with surgical pathology reports in 18 cases (85.7%).
Conclusion: Ultrasonography is feasible and accurate in identifying subtype within postnatally diagnosed pediatric CPAM lesions.

Key words: Lung; Congenital abnormalities; Child; Ultrasonography; Diagnosis

Hongkui Yu, MD, Zhihui Li, MD, Xiao Liu, MD, Weiling Chen, MD, Yuanxiang Wang, MD, Bei Xia, MD. Sonographic Characteristics of Congenital Pulmonary Airway Malformations in Children: A Report of 21 Cases and Review of Literature. Advanced Ultrasound in Diagnosis and Therapy, 2018, 2(2): 133-138.

Figures/Tables 4

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References 17

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